Cogan’s syndrome is a rare inflammatory disorder mainly affecting ocular and audio vestibular system. The typical picture are of interstitial keratitis and sudden onset of Ménière-like attacks (nausea, vomiting, tinnitus, vertigo and hearing loss). A high index of suspicion and multispecialty input will help in the early initiation of therapy and reduce long-term morbidity.
We report a case of this rare entity where the patient had a dramatic response to steroid and immunosuppressive drugs. Considering the variable onset and development of symptoms as well as the lack of specific laboratory tests, the diagnosis of Cogan’s syndrome is also a challenge and is often based on clinical features and response to immunosuppressive treatment.